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A Middle-aged man with Progressive Ophthalmoparesis, Ataxia, and Spastic Paraparesis
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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A 41-Year-Old Woman with Progressive Leg Weakness and Numbness, Dizziness, and Myalgia
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Glutamic Acid Decarboxylase Autoantibodies and Neurological Disorders
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Ataxia-Telangiectasia:An Interdisciplinary Approach to Pathogenesis
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Sarcoidosis of the Nervous System, A Clinical Approach
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Progressive Rubella Panencephalitis
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Hereditary Dentatorubral-Pallidoluysian Atrophy:Clinical and Pathologic Variants in a Family
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Neurological Problems in Endocrine Diseases
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Slowly rogressive Cerebellar Ataxia in a 55-Year-Old Female Patient
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An 82-Year-Old Woman with Subacute Ophthalmoparesis and Ataxia
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A Dizzy Architect
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A 37-Year-Old Man with Involuntary Movements, Gait Disturbance, and Hyperasthesia
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Clinicopathologic Conference, Cerebellar Ataxia, Neuropathy and Vestibular Areflexia Syndrome
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A 47-year-old Man with Rapidly Progressive Ataxia and Vitiligo
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Complex Ataxia
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A 72-year-old Man with a Progressive Cognitive and Cerebellar Syndrome
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Clinicopathologic Conference, Creutzfeldt-Jakob Disease
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A 58-year-old man with Progressive Ptosis and Walking Difficulty
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A 54-year-old woman with Dementia, Myoclonus, and Ataxia
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An 82-year-old man with Worsening Gait
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Spinocerebellar Ataxia Type 2: Clinicogenetic Aspects, Mechanistic Insights, and Management Approaches
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Creutzfeldt-Jakob Disease (Subacute Spongiform Encephalopathy)
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The Autosomal Recessive Cerebellar Ataxias
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Phenotypic Spectrum Associated with Mutations of the Mitochondrial Polymerase y Gene
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Ataxia Associated with Hashimotos Disease: Progressive Non-Familial Adult Onset Cerebellar Degeneration with Autoimmune Thyroiditis
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Paraneoplastic Syndromes
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Clinicopath Conf, Creutzfeldt-Jakob Disease,Case 28-1999
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Fluid Attenuation Inversion Recovery (FLAIR) Images of Dentatorubropalliodoluysian Atrophy:Case Report
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Neurodegeneration and Diabetes:UK Nationwide Study of Wolfram (DIDMOAD) Syndrome
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Cerebral Cortex and Brainstem Involvement in Marinesco-Sjogren Syndrome
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The Marinesco-Sjogren Syndrome Examined by CT, MR, and 18F-2-Fluoro-2-Deoxy-D-Glucose & PET
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Olivopontocerebellar Atrophy in Children:A Report of Seven Cases in Two Families
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Human Cerebellar Hypoplasia, A Syndrome of Diverse Causes
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Juvenile Neuroaxonal Dystrophy:Clinical, Electrophysiological, & Neuropathological Features
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Neurotoxicity of Commonly Used Antineoplastic Agents
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Shrimp Sign in Ataxic Cerebellar Progressive Multifocal Leukoencephalopathy
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More Than a Little Unsteady
NEJM 387:e9, Kraft, A.W.,et al, 2022
Clinical features, prognostic factors, and antibody effects in anti-mGluR1 encephalitis
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Challenging Diagnosis of Gerstmann-Straussler-Scheinker Disease
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Stridor in Multiple System Atrophy
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Progressive Neurological Impairment and an Enhancing Brainstem Lesion in a Middle-Aged Man
JAMA Neurol 76:1397-1398, Gupta, S.,et al, 2019
Cerebellar Ataxia and Hearing Impairment
JAMA Neurol 74:243-244, Lin, C.Y. & Kuo, S.H., 2017
A 13-year-old boy with Chronic Ataxia and Developmental Delay
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Intrathecal 2-hydroxypropyl-�-cyclodextrin Decreases Neurological Disease Progression in Niemann-Pick disease, type C1: a non-randomised, open-label, phase 1-2 trial
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Antibiotic-Associated Encephalopathy
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Extraintestinal Manifestations of Coeliac Disease
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